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Peer-reviewed

Idiopathic neutropenia of infancy: Data from the Italian Neutropenia Registry

Piero Farruggia, Francesca Fioredda, Giuseppe Puccio, Daniela Onofrillo, Giovanna Russo, Angelica Barone, Sonia Bonanomi, Gianluca Boscarol, Andrea Finocchi, Roberta Ghilardi, Paola Giordano, Saverio Ladogana, Giuseppe Lassandro, Laura Luti, Tiziana Lanza, Rosalba Mandaglio, Nicoletta Marra, Baldassare Martire, Elena Mastrodicasa, Milena Motta, Lucia Dora Notarangelo, Marta Pillon, Laura Porretti, Jessica Serafinelli, Angela Trizzino, Fábio C. Tucci, Marinella Veltroni, Federico Verzegnassi, Ugo Ramenghi, Carlo Dufour

American Journal of Hematology · 2018

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Summary

Autoimmune neutropenia of infancy (AIN) is characterized by low risk of severe infection, tendency to spontaneously resolve and typically onset at ≤4-5 years of age; it is due to auto-antibodies whose detection is often difficult. In case of negativity of 4 antineutrophils autoantibody tests, after having excluded ethnic, postinfection, drug induced, or congenital neutropenia, according to the Italian guidelines the patients will be defined as affected by "idiopathic neutropenia" (IN). We describe the characteristics of 85 IN patients enrolled in the Italian neutropenia registry: they were compared with 336 children affected by AIN. The 2 groups were clinically very similar and the main differences were detection age (later in IN), length of disease (longer in IN) and, among recovered pati

Source type
Peer-reviewed study
DOI
10.1002/ajh.25353
Catalogue ID
SNmojolia6-p40usa
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