Pulse Brain · Growing Health Evidence Index
Tier 3 — Observational / field trialPeer-reviewed

Un caso familiar de microduplicación distal 22q11.2

L Domingo Comeche, MJ Rivero Martín, S de las Heras Ibarra, Mary C. Martin, B García Pimentel

Acta pediátrica española/Acta pediátrica española · 2020

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Summary

This case report describes two family members with distal 22q11.2 microduplication, a rare chromosomal disorder with expanding clinical recognition. The index case presented as a premature neonate with early sepsis, bronchopulmonary dysplasia, patent ductus arteriosus, severe hyperbilirubinaemia requiring exchange transfusion, rickets, and bilateral sensorineural hearing loss, with subsequent findings of short stature and dysmorphic features including macrocephaly, broad forehead, epicanthus, and brachydactyly. The paper appears to contribute to the growing literature on the phenotypic spectrum of this condition through familial presentation.

UK applicability

This case report has limited direct relevance to UK farming, soil health, or food systems. It may inform neonatal screening protocols and genetic counselling services in UK paediatric practice, but falls outside Vitagri's core research focus.

Key measures

Clinical phenotype, neuroimaging findings, genetic testing results, developmental milestones, dysmorphic features

Outcomes reported

The study documents clinical presentation and phenotypic features of distal 22q11.2 microduplication across two family members, including neonatal complications and developmental abnormalities.

Theme
General food systems / other
Subject
Other / interdisciplinary
Study type
Research
Study design
Case report / Family pedigree study
Source type
Peer-reviewed study
Status
Published
Geography
Spain
System type
Human clinical
Catalogue ID
BFmohg5drm-t50o7f

Topic tags

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